Outcomes after surgical treatment of children with partial anomalous pulmonary venous connection to the superior vena cava

  • Yoshie Ochiai, Kyusyu Koseinenkin Hospital, Japan
  • Yutaka Imoto, Kyusyu Koseinenkin Hospital, Japan
  • Masato Sakamoto, Kyusyu Koseinenkin Hospital, Japan
  • Akira Sese, Kyusyu Koseinenkin Hospital, Japan
  • Mamie Watanabe, Kyusyu Koseinenkin Hospital, Japan
  • Tetsuji Yuge, Kyusyu Koseinenkin Hospital, Japan
  • Takuro Ohno, Kyusyu Koseinenkin Hospital, Japan
  • Kunitaka Joo, Kyusyu Koseinenkin Hospital, Japan
  • Objective: Repair of anomalous pulmonary venous connection (PAPVC) to the superior vena cava (SVC) using an internal patch may be complicated by obstruction of the SVC or pulmonary veins (PV), or both, and sinus node dysfunction. Since 1996, we have adopted the Williams’ method in which the SVC is divided and the proximal end is anastomosed to the right atrial appendage, and the distal SVC serves as a conduit for pulmonary drainage to the left atrium through the atrial septal defect (ASD). We retrospectively compared the results of the patch repair versus the Williams’ method. Methods: Between 1985 and 2007, 19 patients who underwent surgical treatment of PAPVC to the SVC were included. Mean age was 10.5 years (range, 1.5 to 41). In our early 7 patients, internal tunnel patch was used to close the ASD and reroute the anomalous PV into the left atrium, and another patch was used for enlargement of SVC and right atrial wall (double patch method). One patient was treated by only an internal tunnel patch, and 11 patients underwent the Williams’ method. Results: There were no early or late deaths. Postoperative obstruction of the SVC and the right superior PV was recognized in two patients who underwent the double patch method. One of these patients showed sick sinus syndrome. In contrast, 11 patients with the Williams’ method did not show sinus node dysfunction or any obstruction of SVC or PV. Conclusions: The Williams’ method appears to be safe and effective procedure without any complication.