Anomalous systemic venous connection causing cyanosis – surgical options

  • Dr Prashantkumar Shah, miot children cardiac care, India
  • Dr R Satish, miot children cardiac care, India
  • Dr K Sivakumar, miot children cardiac care, India
  • Dr Robert Coelho, miot children cardiac care, India

    • INTRODUCTION:
    Anomalous systemic venous connection is very rare and this anomaly causing cyanosis is rarer. All possible causes we have reviewed and described our experience.

    MATERIAL AND METHODS:
    Single institute study from March 2007- till date. SVC anomaly includes B/L SVC with large unroofed coronary sinus – 2 patients.(group-1)
    Common atrium with LSVC to roof of LA – 2 patients.(group-2)
    Isolated RSVC to LA with PAPVC – 1 patient.(group-3)
    IVC to LA after ASD closure – 2 patients.(group-4)
    Surgery performed in all patients with roofing of coronary sinus with gortex patch in group1, baffling of LSVC to RA with autologous pericardial patch in group 2.Direct anastamosis of RSVC to RA in group3 without cardiopulmonary bypass. Anastamosis of LSVC to RA with interposition of 18mm PTFE tube graft – 1 patient.
    In group 4 Baffling of IVC to RA with pericardial patch after excising previous patch.

    CONCLUSION:
    Various anomalies of SVC and IVC can be delt with appropriate surgical technique with good surgical outcome.