Unlike true sequestration, the patient with pseudo-sequestration has normal bronchial distribution and intact involved lung parenchyma, as termed anomalous systemic arterial supply to the normal basal segments of the lung. Therefore, in order to conserve optimal lung function, anatomical repair should be considered. However, pseudo-sequestration has been treated by surgical lobectomy or coil embolization.
Herein we present a case of 6-year-old boy with pseudo-sequestration in the left lower lung. We performed an anatomical anastomosis between the anomalous vessel and the pulmonary artery via a left thoracotomy. Six months after the operation, a lung perfusion scan showed a significant improvement in the affected lobe. Our case suggests clinical efficacy of the anatomical repair for this rare abnormality.