Diagnosis and Prognosis in Double Outlet Right Ventricle

  • Dr Kazim Oztarhan, Istanbul Bakirkoy Maternity and Children Diseases Hospital, Department of Pediatric Cardiaology, Turkey
  • Dr Ali Gedikbasi, Istanbul Bakirkoy Maternity and Children Diseases Hospital, Department of Maternal and Fetal Medicine, Turkey
  • Dr Alper Guzeltas, Istanbul Bakirkoy Maternity and Children Diseases Hospital, Department of Pediatric Cardiaology, Turkey
  • Dr Gokhan Yildirim, Istanbul Bakirkoy Maternity and Children Diseases Hospital, Department of Maternal and Fetal Medicine, Turkey
  • Dr Yavuz Ceylan, Istanbul Bakirkoy Maternity and Children Diseases Hospital, Department of Maternal and Fetal Medicine, Turkey

    • Objective:
    The aim of this study was to examine prenatal diagnosis of double outlet right ventricle, associated anomalies, and prognosis of each case.
    Method:
    Medical records of fetuses with DORV were reviewed who had fetal echocardiography at our institution from 2002 to 2008. Pre- and postnatal diagnosis and outcome were compared and evaluated.
    Result:
    Twenty-two fetuses were diagnosed with DORV. The pregnancy was terminated in seven cases (32.8%). Three cases had chromosomal abnormalities, three cases hypoplastic left ventricle and one case encephalocele. Accurate prenatal diagnosis of the ventricular septal defect (VSD), outflow obstruction, and great artery relationship was achieved in 14 of 16 cases (87.5%). Only two of 13 live born cases survived beyond six months.
    Conclusion:
    The overall prognosis for fetuses with DORV is poor. DORV is found in fetuses with a huge spectrum of associated anomalies cardiac and extracardiac anomalies. Careful assessment by fetal echocardiography can determine important anatomic details with adequate correctness for precise counseling.