We report a 12 years old male patient who has truncus arteriosus, large ventricular septal defect, pulmonary hypertension and successfully underwent corrective surgery.
This patient was admitted to another Pediatric Cardiology Center, diagnosed as truncus arteriosus and pulmonary stenosis (60 mmHg systolic gradient between the truncal artery and the pulmonary artery) when he was three months old and lost the following. The patient was evaluated with echocardiography and cardiac catheterization at 12 years old in our center and diagnosed as truncus arteriosus, large ventricular septal defect and pulmonary hypertension with echocardiography. Pulmonary stenosis was not detected and pulmonary vascular resistance showed significant reversibility with oxygen administration at cardiac catheterization. The patient successfully underwent surgical correction. Postoperative cardiac catheterization showed normal pulmonary arterial pressure. The patient is in good condition after one-year follow-up.
The reversibility of pulmonary vascular resistance and successful surgical correction may be due to the pulmonary stenosis during infancy.