Surgical correction of an anomalous origin of the left pulmonary artery branch from the ascending aorta in an infant with sub aortic obstruction
Objective. The aim of this study is to describe a clinical case of anomalous origin of the left pulmonary artery branch from the ascending aorta, and to present a current literature review of this rare disease.
Methods. A 2 year-old infant was referred to our institution for surgical correction of sub aortic obstruction. The non invasive investigation disclosed a right aortic arch anatomy with left ventricle outflow tract obstruction due to sub aortic membrane associated with an anomalous origin of the left pulmonary artery branch from the ascending aorta. Immediately after diagnosis, the patient underwent a total surgical correction of the defects, including simultaneous anastomosis of the left pulmonary artery to the pulmonary trunk.
Results. Results of the surgical repair of this case were successful. We also present a literature review of the incidence, pathophysiological, clinical, diagnostic, and surgical characteristics of this rare disease.
Conclusions. Although anomalous origin of the left pulmonary artery branch from the ascending aorta is a rare disease, successful results can be obtained when early diagnosis and opportune total surgical corrections are performed.