Double outlet right ventricle (DORV) with subpulmonary ventricular septal defect (the Taussig-Bing heart): analysis of surgical outcome and predictors of prognosis
Materials and Methods: From August 1995 to August 2008. There were 34 Taussig-Bing complex in NTUH, 10 female and 24 male. The location of VSDs were subpulmonary, diameter ranging from 3mm to 20mm. Fourteen cases were associated with coarctation of aorta or hypoplastic aortic arch (41.1%). Twenty-nine cases received definite surgery (85.3%), either arterial switch operation (ASO) with VSD repair (26, 89.9%), or Kawashima procedure with Rastelli conduit(3, 10.1%). The rest 5 partiers had complex intracardiace anomalies(1 with severe LVOTO and 3 hypoplastic LV) and Eisemenger reaction. They all were excluded. Patients with definite repairs were separated into 2 groups: before 1999 (Group I) and after 1999 (group II). The operation results and long-term follow-up were compared among group I and II. Factors such as VSD size, associated anomaly, age at operation, presence of subaortic or subpulmonary stenosis were analyzed. Results: Before 1999, there were 14 cases in Group I receiving definite surgery, including ASO(12) or Kawashima procedure with Rastelli conduit(2), and there were 7 early mortality within 30 days post-op(50%). After 1999, there were 15 Taussig-Bing cases receiving definite surgery: ASO in 14 cases and Kawashima procedure with Rastelli conduit in 1 case. There was 2 early mortality case (13.3%). The long-term survival was steady in OPD follow-up, except for one sudden death case in groupI 4 years after operation. Hypoplastic LV and restrictive VSD are the risk factors.Conclusions:Arterial switch operation will be the surgical treatment of choice with satisfactory result for the Taussig-Bing anomaly.