Pprenatal echocardiographic findings of MAPCAs(Major Aortopulmonary Collaterals) : Two Case Reports

  • Dr Da-Hye Ju, Department of Obstetrics and Gynecology,University of Ulsan College of Medicine, Asan Medical Center, Seoul, Korea, Korea
  • Dr Hye-Sung Won, Department of Obstetrics and Gynecology,University of Ulsan College of Medicine, Asan Medical Center, Korea
  • Dr In-Sook Park, Department of Pediatric Cardiology, Asan Medical Center, University of Ulsan College of Medicine, Korea
  • Dr Pil Ryang Lee, Department of Obstetrics and Gynecology,University of Ulsan College of Medicine, Asan Medical Center, Seoul, Korea, Korea
  • Dr Ahm Kim, Department of Obstetrics and Gynecology,University of Ulsan College of Medicine, Asan Medical Center, Korea

    • Pulmonary atresia(PA) and ventricular septal defect(VSD) associated major aortopulmonary collateral arteries(MAPCAs) is uncommon complex congenital heart anomaly as a severe form of tetralogy of Fallot. This anomaly occurs in 1.5% of patients with congenital heart disease, and 15~20% of tetralogy of Fallot. MAPCAs are wide connection arteries originated from the descending aorta, the arcus aorta or the subclavian artery. The majority of untreated patients present with severe congestive heart failure and respiratory distress. Prenatal diagnosis of PA and VSD associated with MAPCAs is important to counsel parents to outcome. We present two cases of PA and VSD associated with MAPCAs examined prenatally by fetal echocardiography.