_{Obgective: evaluation of the structure and results of surgical treatment in adults patients with CHD.
METHODS: Since 1985 919 adult patients with CHD were admitted to the National research center of surgery of Russian academy of medical science. Age ranged from 16 to 71 years (mean = 38). Four groups of patients were revealed: 1. primary surgical intervention (n=701); 2. the patients underwent reoperations due to some residual complications (n=68); 3. CHDs that do not require intervention (n=115) 4. CHDs that are inoperable (n=35).
Among the 701 patients who underwent primary surgical correction 210 had an ASD, 85 VSD, 110 - LVOT pathology, 103 TOF (48,5% of them had previous palliative procedure), 82 an uncomplicated aortic coarctation, 30 PDA, 41 partial AVSD, 18 pulmonary stenosis, 12 partial APVC, 10 DORV with PS.
RESULTS: overall operative mortality in the 1-st group was 3,8%. The preoperative risk factors were high pulmonary hypertension, cyanosis, mayor aorta-pulmonary collateralis, heart failure, pulmonary artery branches deformation. Overall operative mortality for reintervential surgery was 3,3%. The third group patients were asymptomatic and did not require treatment. The patients of fourth group with Eisenmenger syndrome (n=23), were cyanotic but did not undergo surgery due to high operative risk.
Conclusion: Grown-ups with congenital heart disease are an increasingly important group of patients. In Russian Federation significant numbers of adults with operated and unoperated congenital heart disease do exist. Many of them require reoperations because of late complications or residual defects, correction after palliation, or heart transplantation.}