Objective: Investigate the incidence and the diagnoses time of aortic valve stenosis (AVS) and subaortic stenosis (SUBAS) in combination with aortic coarctation (COA). Methods: A retrospective review of 36 patients with COA who were evaluated between 2003 and 2008 in a pediatric cardiology service. Results: At the time the COA was diagnosed, median age was 25 months (range 6 days to 10 years 3 months) among these patients 61,1% were male. The median age, when the AVS was diagnosed, was 21 months (range 2 days to 11 years 3 months) and for SUBAS the age was 41 months (range 85 days to 8 years). Within the 13 patients who presented AVS, 5 of them were diagnosed with COA at the same moment, 4 others had AVS identified before COA and 4 after the first evaluation. For the SUBAS, 7 patients were diagnosed after the COA and just 1 at the same time. Twenty seven pediatric patients underwent COA surgery, 14,8% were considered neonates, 29,6% infants and 55,6% children. There was no death. Balloon angioplasty was the treatment in 2 patients with native COA, one of them had to undergo a surgery later. Three patients needed the angioplasty due to recoarctation. Conclusion: In the patients with COA, the incidence of associated AVS was 36,1% and the SUBAS was 22,2%, presenting itself higher than dades found in literature. The early diagnoses was made in 9 of the patients with AVS (69,2%). Therefore the SUBAS diagnose was late.